Clin2
NCT05092685Possibly a fitRecruiting

Gene therapy trial for children with OTC ammonia build-up

Ornithine Transcarbamylase Deficiency

Part of Brain & nervous system, Genetic & congenital, Hormones & metabolism clinical trials.

This early-phase study tests an AAV gene therapy meant to reduce ammonia levels in children with ornithine transcarbamylase (OTC) deficiency. It’s designed to slow or stop ammonia-related harm, while also carefully monitoring safety for years.

Summary written for real people, not researchers, by Clin2.

Phase
Phase 1/Phase 2
Enrollment
12 people
Ages
birth to 16 years
Study type
Interventional

Who can take part

  • You (or your child) must be 0–16 years old for study enrollment, with 6–16 for dose-adding parts
  • OTC deficiency must be confirmed by a blood/tissue test or genetic testing
  • The condition must be severe, meaning a restricted protein plan and at least one ammonia-lowering medicine
  • Ammonia level before gene therapy must be below 100 µmol/L and not abnormal compared with past stable readings
  • You must have a stable protein allowance and a stable ammonia-lowering medicine dose for the last 4 weeks
  • You must agree to long-term safety follow-up for 4 more years

View the official record on ClinicalTrials.gov

Quick eligibility check

Answer a few plain-language questions, based on this study's own requirements, to get a preliminary sense of fit.

Similar studies

Other trials that look related to this one.

NCT06255782Recruiting· Phase 3
Gene therapy study for baby boys with severe OTC deficiency

This trial tests a gene therapy called ECUR-506 for baby boys under 9 months old with a severe form of OTC deficiency. The goal is to see if it can help their bodies process ammonia better, reducing the need for a strict protein-restricted diet and medications.

Los Angeles, California
NCT06488313Recruiting· Phase 2
Study of ARCT-810 for people with OTC deficiency

This trial tests an experimental medicine called ARCT-810 for people with Ornithine Transcarbamylase (OTC) deficiency, a condition that affects the liver's ability to remove ammonia from the body. The study aims to see if ARCT-810 can help lower ammonia levels safely.

Chevy Chase, Maryland
NCT05765981Recruiting· Early Phase 1
Testing a gene therapy for AADC deficiency in young children

This early-stage trial tests VGN-R09b, a gene therapy, given to children with AADC deficiency who are not doing well on standard medicines. It aims to improve symptoms and quality of life by addressing the underlying cause of AADC deficiency.

Shanghai, No. 1678, Dongfang Road, Pudong New Area, Shanghai
NCT07665021Recruiting· Phase 1/Phase 2
Gene therapy for children with severe bone disease

This trial tests a gene therapy that uses a child's own stem cells to treat autosomal recessive osteopetrosis (a genetic bone disease). It aims to improve bone health and reduce complications like fractures and vision loss.

Milan, Italy
NCT06217861Recruiting· Phase 1
Gene therapy for children with GA-1 not helped by standard care

This trial tests a new gene therapy (VGM-R02b) for children with Glutaric Acidemia Type 1 (GA-1) whose symptoms are not well controlled by standard treatment. The goal is to see if the therapy is safe and can help improve neurological symptoms.

Hangzhou, Zhejiang
NCT07173153Enrolling by invitation· Phase 1/Phase 2
Gene therapy study for SLC6A1 genetic disorder

This trial tests a gene therapy for people with a specific mutation (S295L) in the SLC6A1 gene, which causes a neurodevelopmental disorder. The therapy aims to correct the genetic issue, and participants will be monitored closely for safety and effectiveness.

Columbus, Ohio

Hear when a new Ornithine Transcarbamylase Deficiency trial opens

We’ll email you when one opens — at most once a week, no account needed, unsubscribe anytime.